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Literatura académica sobre el tema "Hypoplastic heart syndromes"

Autor: Grafiati

Publicado: 11 de marzo de 2023

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Artículos de revistas sobre el tema "Hypoplastic heart syndromes"

1

REIS, PATRICIA M., MARGARET R. PUNCH, EDWARD L. BOVE y COSMAS J. M. VAN DE VEN. "Outcome of Infants With Hypoplastic Left Heart and Turner Syndromes". Obstetrics & Gynecology 93, n.º 4 (abril de 1999): 532–35. http://dx.doi.org/10.1097/00006250-199904000-00012.

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Reis, P. "Outcome of infants with hypoplastic left heart and turner syndromes". Obstetrics & Gynecology 93, n.º 4 (abril de 1999): 532–35. http://dx.doi.org/10.1016/s0029-7844(98)00462-1.

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Caliebe, A., J. Hansen, K. Becker, U. M. M. Bauer, H. H. Kramer y M. P. Hitz. "Types of Recognisable Syndromes Observed in Patients with Hypoplastic Left Heart Syndrome (HLHS)". Thoracic and Cardiovascular Surgeon 65, S 02 (2 de febrero de 2017): S111—S142. http://dx.doi.org/10.1055/s-0037-1599031.

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Turturro, Francesco, Cosma Calderaro, Antonello Montanaro, Luca Labianca, Giuseppe Argento y Andrea Ferretti. "Isolated Asymptomatic Short Sternum in a Healthy Young Girl". Case Reports in Radiology 2014 (2014): 1–3. http://dx.doi.org/10.1155/2014/761582.

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Congenital sternal defects are rare deformities frequently associated with other anomalies of the chest wall and other organ systems. Although pectus excavatum, pectus carinatum, and cleft sternum can present as isolated deformity, in most cases they are associated with heart and inner organs anomalies and described as symptoms of syndromes like Marfan syndrome, Noonan syndrome, Poland anomaly, and Cantrell pentalogy. In contrast, the etiology of an isolated defect is not well understood. We observed a short sternum (dysmorphic manubrium, hypoplastic body, and complete absence of the xiphoid process) in a completely asymptomatic 13-year-old woman. A comprehensive instrumental exams panel was performed to exclude associated anomalies of the heart and of the other organ systems. The patient was completely asymptomatic and she did not need any medical or surgical treatment. To our knowledge, this is the first case of isolated short sternum reported in literature.

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5

Mohamed Ahmed, Eltayeb, Alexandru Ciprian Visan, Graham Stuart y Serban Stoica. "Aortic root and hemiarch replacement in a patient with Loeys–Dietz and hypoplastic left heart syndromes†". Interactive CardioVascular and Thoracic Surgery 26, n.º 2 (11 de octubre de 2017): 346–47. http://dx.doi.org/10.1093/icvts/ivx336.

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Annigeri, Rajeshwari G., V. V. Subba Reddy, G. P. Mamatha, Manisha Jadhav y P. Poornima. "Ellis-van Creveld syndrome affecting siblings: A case report and review". CODS Journal of Dentistry 6, n.º 1 (2014): 40–44. http://dx.doi.org/10.5005/cods-6-1-40.

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Abstract Ellis-van Creveld syndrome (EVC) is a genetic disorder that was first described by Richard Ellis and Simon van Creveld in 1940. EVC is a rare autosomal recessive disease resulting from a genetic defect located in chromosome 4p16. The name chondroectodermal is used as it affects both the skeleton (chondro) and the skin (ectoderm). The four principal characteristics are chondrodysplasia, polydactyly, ectodermal dysplasia and congenital heart defects. The patients have small stature, short limbs, fine sparse hair and hypoplastic nails. The orofacial manifestations include multiple gingivolabial musculofibrous frenule, dental anomalies like hypodontia associated with malocclusion. This entity can be diagnosed at any age, even during pregnancy. The differentiation should be made between Asphyxiating Thoracic Dysplasia (Jeune syndrome) and other orofaciodigital syndromes. A multidisciplinary approach is required to manage this condition. We are reporting a rare clinical entity of chondroectodermal dysplasia with classical signs affecting siblings who reported to the Department of Oral Medicine and Radiology with review of its literature. How to cite this article Mamatha GP, Manisha J, Rajeshwari GA, Poornima P, Subba Reddy VV. Ellis-van Creveld syndrome affecting siblings – A case report and review. CODS J Dent 2014;6;40-44

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Anderson, Robert H., Audrey Smith y Andrew C. Cook. "Hypoplasia of the left heart". Cardiology in the Young 14, S1 (febrero de 2004): 13–21. http://dx.doi.org/10.1017/s1047951104006249.

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The lesion that, nowadays, is most usually described as “hypoplastic left heart syndrome”, was initially described in terms of “hypoplasia of the aortic outflow tract complex”.1 Sporadic cases with aortic atresia, an intact ventricular septum, and gross hypoplasia of the left ventricle, had been described long before, but it was Noonan and Nadas, in a landmark study, who coined the term “hypoplastic left heart syndrome”.2 The paediatric cardiac community has now accepted this term uniformly, although as we will see, problems remain with regard to precisely which malformations should be included within the “syndrome”. The term itself, nonetheless, is not beyond criticism. This is because, for those working in the genetic community, a “syndrome”, by definition, is a constellation of anomalies afflicting multiple systems of organs. The so-called “hypoplastic left heart syndrome”, however, almost always involves only the heart and the great arteries. Thus, according to the geneticists, it should not strictly be described as a “syndrome”, although the Nomenclature committee of the International Coding Project have marshalled arguments in favour of the term. In this review, nonetheless, we will skirt these problems with the use of “syndrome”, and simply describe the morphology as seen in patients unified because they have hypoplasia of the left heart.

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Jessie, Evangelista E., Mary M. Ruisi, Daniel Green, Rachel Burt, Jaclyn Davis, Regina A. Macatangay, Farid Boulad et al. "Radioulnar Synostosis-Hematology (RUS-H) Syndrome: Description of the New Syndrome and Comparison to Similar Syndromes". Blood 120, n.º 21 (16 de noviembre de 2012): 1100. http://dx.doi.org/10.1182/blood.v120.21.1100.1100.

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Abstract Abstract 1100 Congenital radioulnar synostostis (RUS) is a rare anomaly characterized by fusion of the radius and ulna. RUS occurs more frequently in males than females, and is bilateral in 50% of cases. Since 1793, there have been > 400 cases reported. Literature review revealed 7 rare syndromes with RUS and hematologic problems including our newly named RUS-H Syndrome: 1) Diamond-Blackfan Anemia (DBA) associated with normochromic, macrocytic anemia in early infancy and erythroblastopenia; 2) Amegakaryocytic Thrombocytopenia Radioulnar Syndrome (ATRUS, HoxA11 mutation) with thrombocytopenia since birth requiring stem-cell transplantation; 3) IVIC Syndrome with mild thrombocytopenia and leukocytosis; 4) WT Syndrome involving a wide array of hematologic abnormalities including easy bruising, hypoplastic anemia, pancytopenia, Acute Lymphoblastic Leukemia (ALL), and Acute Myeloblastic Leukemia (AML); 5) Cohen Syndrome with neutropenia and fluctuating thrombocytopenia; 6) Noonan Syndrome with abnormal bleeding and easy bruising; and 7) RUS-H Syndrome (not involving HoxA11 mutations) associated with a spectrum of hematologic abnormalities including easy bruising, recurrent epistaxis, neutropenia, thrombocytopenia, ALL and aplastic anemia. This is a subsequent report to our ASH 2010 abstract. All 7 syndromes are associated with hand abnormalities. Six of the 7 syndromes (not Cohen) are associated with hearing loss/ear abnormalities. Four syndromes (DBA, ATRUS, WT, and RUS-H) have an increased risk of hematological malignancy. DBA, IVIC, Cohen, and Noonan have abnormalities of the eye and genitourinary system. DBA, WT, Cohen, and Noonan Syndromes are associated with dysmorphic facial features. ATRUS, IVIC, Cohen, and Noonan Syndromes all exhibit lower limb abnormalities. DBA, Cohen, Noonan, and RUS-H are associated with short stature. DBA, IVIC, Noonan, and RUS-H Syndromes are associated with kidney abnormalities and structural heart defects. Three Syndromes (DBA, IVIC, and Cohen) have cranial abnormalities. DBA IVIC, and Noonan Syndrome have structural defects of the shoulder. IVIC, Cohen, and Noonan Syndromes are associated with spinal anomalies. Two Syndromes (DBA and Noonan Syndrome) are associated with liver, spleen, and neck abnormalities. Cohen and Noonan Syndrome are associated with developmental delays. Lastly, WT and Noonan Syndrome are associated with skin abnormalities (Figure 1). This abstract highlights the association of RUS, other congenital abnormalities, and hematologic problems in previously described syndromes and in the novel RUS-H Syndrome. DBA, Cohen, and Noonan Syndrome are the most common of the 7 syndromes, with DBA estimated at 5 per 1,000,000; Cohen Syndrome predicted to have a prevalence of <1,000; and Noonan Syndrome predicted to have a prevalence of <1 in 2,500; however, RUS in DBA, Cohen, and Noonan Syndrome is limited to case reports. RUS-H Syndrome has been identified in 12 families in the United States, Canada, and England. IVIC and WT Syndromes have been reported in 4 families total, and ATRUS with an identified HoxA11 mutation has been reported in at least 2 families. Since RUS may often be missed on routine physical examination, we recommend specific evaluation of pronation/supination in patients with hematological problems of unknown etiology. Additionally, we recommend that a targeted genetic panel be developed to detect mutations that are known for syndromes involving RUS, blood abnormalities, and other similar orthopedic entities that have cross-over manifestations like Thrombocytopenia-Absent Radii (TAR) Syndrome. This panel might consist of mutations associated with DBA (RPL5, RPL11, RPL35A, RPS7, RPS10, RPS17, RPS19, RPS24, and RPS26 mutations), with ATRUS (HoxA11 mutation), with IVIC Syndrome (SALL4 mutations), with Cohen Syndrome (8q22.2q22.3/COH1 deletion), with Noonan Syndrome (PTPN11, SOS1, RAF1, KRAS, NRAS, and BRAF mutations) and with TAR Syndrome (RBM8A null allele and noncoding SNP). The causative mutations of WT and RUS-H Syndromes have yet to be discovered. Genetic analysis of 6 of the 12 families with RUS-H Syndrome did not reveal a HoxA11 mutation. Broader sequencing techniques are underway for all 12 families in our RUS-H cohort, with hopeful detection of a new candidate gene as the unifying causative factor for the abnormalities in limb formation and hematopoiesis. Disclosures: Bussel: Ligand: Membership on an entity's Board of Directors or advisory committees, Research Funding; Immunomedics: Research Funding; IgG of America: Research Funding; Genzyme: Research Funding; GlaxoSmithKline: Family owns GSK stock, Family owns GSK stock Other, Membership on an entity's Board of Directors or advisory committees, Research Funding; Cangene: Research Funding; Amgen: Family owns Amgen stock Other, Membership on an entity's Board of Directors or advisory committees, Research Funding; Eisai: Membership on an entity's Board of Directors or advisory committees, Research Funding; Shionogi: Membership on an entity's Board of Directors or advisory committees, Research Funding; Sysmex: Research Funding; Portola: Consultancy.

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Tchervenkov, Christo I., Richard Tang y Jeffrey P. Jacobs. "Hypoplastic Left Ventricle: Hypoplastic Left Heart Complex". World Journal for Pediatric and Congenital Heart Surgery 13, n.º 5 (septiembre de 2022): 631–36. http://dx.doi.org/10.1177/21501351221116016.

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Hypoplastic left heart syndrome (HLHS) without intrinsic valvar stenosis or atresia is synonymous with the term hypoplastic left heart complex (HLHC) and is defined as a cardiac malformation at the milder end of the spectrum of HLHS with normally aligned great arteries without a common atrioventricular junction, characterized by underdevelopment of the left heart with significant hypoplasia of the left ventricle and hypoplasia of the aortic or mitral valve, or both valves, in the absence of intrinsic valvar stenosis or atresia, and with hypoplasia of the ascending aorta and aortic arch. This article describes the definitions, nomenclature, and classification of HLHC; the indications and contraindications for biventricular repair of HLHC; the surgical treatment of HLHC; and the associated outcomes.

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Morell, Victor O., James A. Quintessenza y Jeffrey P. Jacobs. "Biventricular repair in the management of hypoplastic left heart syndrome". Cardiology in the Young 14, S1 (febrero de 2004): 101–4. http://dx.doi.org/10.1017/s1047951104006390.

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Hypoplastic left heart syndrome is the term introduced by Noonan and Nadas1to describe a spectrum of cardiac anomalies characterized by varying degrees of significant underdevelopment of the left heart and aortic arch. These cardiac anomalies include mitral valvar disease, left ventricular hypoplasia, aortic stenosis at subvalvar, valvar, and supravalvar levels, hypoplasia of the ascending aorta and aortic arch, and aortic coarctation. Although descriptive, hypoplastic left heart syndrome suffers from being a very unspecific term, since it encompasses multiple degrees and combinations of abnormalities involving the left sided structures. In an attempt to provide gradings of severity, Kirklin and Barratt-Boyes2categorized these patients falling into the syndrome into four classes, according to whether obstruction was found at one, two, or more levels, or whether there is aortic atresia. Then, in 1998, Tchervenkov and colleagues3introduced the term hypoplastic left heart complex to describe a set of patients falling within the spectrum of hypoplasia of the left heart, but in the absence of intrinsic aortic or mitral valvar stenosis, this concept subsequently being endorsed by the International Committee established by the Society of Thoracic Surgeons, together with the European Association of Cardiothoracic Surgery, to rationalize the approach to nomenclature and databases.4The analysis offered by Tchervenkov et al.3showed that, in certain circumstances, there are potentially patients considered to have hypoplasia of the left heart who might be candidates for biventricular repair. If this is the case, then it is important to establish how this subset can be recognized, and how they are best treated.

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Tesis sobre el tema "Hypoplastic heart syndromes"

1

Salih, Caner. "The ventricular ultrastructure in hypoplastic left heart syndrome". Thesis, Imperial College London, 2005. http://ethos.bl.uk/OrderDetails.do?uin=uk.bl.ethos.417242.

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Phillips, Helen M. "Molecular genetic investigation of hypoplastic left heart syndrome". Thesis, University of Newcastle Upon Tyne, 2002. http://ethos.bl.uk/OrderDetails.do?uin=uk.bl.ethos.246638.

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3

Perez, Ramirez Leilanie. "Lymphopenia in infants with Hypoplastic Left Heart Syndrome". University of Cincinnati / OhioLINK, 2015. http://rave.ohiolink.edu/etdc/view?acc_num=ucin1439305259.

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Renforth, Glenn Lee. "A molecular genetic investigation of hypoplastic left heart syndrome". Thesis, University of Southampton, 2005. http://ethos.bl.uk/OrderDetails.do?uin=uk.bl.ethos.431956.

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5

Bellsham-Revell, Hannah. "Pathophysiology of the systemic right ventricle in hypoplastic left heart syndrome". Thesis, King's College London (University of London), 2013. https://kclpure.kcl.ac.uk/portal/en/theses/pathophysiology-of-the-systemic-right-ventricle-in-hypoplastic-left-heart-syndrome(62ed8eec-549c-4e58-88c7-60a2a959f7e6).html.

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Background: Hypoplastic left heart syndrome (HLHS) describes a spectrum of underdevelopment of the left heart, rendering it incapable of supporting the systemic circulation. Improved results from Norwood palliation mean more children are surviving into later childhood. The assessment of right ventricular (RV) function is an important prognostic factor, but is complicated by wide heterogeneity and complex geometry. Novel MRI and echocardiographic techniques are non-invasive and may offer insight into the pathophysiology of the systemic RV. Methods: Current methods for assessing the RV were reviewed. MRI and echocardiography were used and compared prospectively in HLHS patients to investigate RV performance and changes in ventricular volumetry across the palliative stages. The novel approach of pre-Fontan assessment using MRI and central venous pressure (CVP) measurement alone was compared to the current literature. Results: Echocardiographic subjective assessment of RV function in HLHS had little concordance with MRI ejection fraction, showing the limitation of using this method alone. MRI demonstrated significant RV volume unloading after hemi- Fontan, with a shift of the Starling curve suggesting improved contractility. The novel pre-Fontan assessment showed no difference in outcomes from the published literature. Tissue Doppler time intervals were significantly different in HLHS patients compared to normal hearts. Differences were also seen in tissue Doppler indices and speckle tracking derived strain between those with a significant residual left ventricle and those without Conclusions: Novel MRI and echocardiographic techniques give unique and reproducible insights into the morphologic and functional development of the systemic RV across the stages of surgical palliation. Important differences between the morphological subtypes were also noted. Based on this MD thesis, reliable, easy to use, reproducible and non-invasive screening tools have been established, validated and used for longitudinal follow-up. These techniques may also lead to improved follow-up: predicting, or possibly preventing systemic RV failure.

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6

Cheatham, Sharon Laneau. "Neurodevelopmental Outcomes in Infants with Hypoplastic Left Heart Syndrome after Hybrid Stage I Palliation". The Ohio State University, 2012. http://rave.ohiolink.edu/etdc/view?acc_num=osu1354649654.

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Crawford, Daniel. "Outcomes for the Hybrid Approach to First State Treatment of Hypoplastic Left Heart Syndrome". Thesis, The University of Arizona, 2018. http://hdl.handle.net/10150/627198.

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A Thesis submitted to The University of Arizona College of Medicine - Phoenix in partial fulfillment of the requirements for the Degree of Doctor of Medicine.
BACKGROUND & SIGNIFICANCE Hypoplastic left heart syndrome (HLHS) is a congenital condition that involves hypoplasia or atresia of left heart structures. Treatment requires three separate interventions, and the “hybrid” procedure is a less invasive alternative to the initial open-heart operation. This approach has become favorable for certain patients in recent years, but there is a need to better understand the outcomes and the factors that influence the outcomes for hybrid Stage 1 palliation of HLHS.

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Trippenbach, Teresa Aniela. "Small hearts - grand matters. The ethics of neonatal treatment with unknown long-term outcome : the case of hypoplastic left heart syndrone". Thesis, McGill University, 2001. http://digitool.Library.McGill.CA:80/R/?func=dbin-jump-full&object_id=29405.

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Ethical decisions about medical care of infants is based on the by proxy evaluation of the infants' best interests. Since parents and physicians may have different points of reference, conflicts may arise during the decision-making process. The decision about the infant's well being becomes even more complex when high risk treatment with an uncertain long-term outcome is considered. Surgical palliation of hypoplastic left heart syndrome (HLHS) is an example of such a treatment. I use this example in my discussion on the relevant ethical issues and possible roots of conflicts between the decision-makers.
I argue that as long as long-term survival rates are variable, and the survivors' quality of life remains uncertain, palliative surgery for HLHS should not be obligatory. Rather, the parents should be informed not only about the existing treatments but also about the non-treatment option, and what each option may imply for the infant, parents and the family.

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Vorisek, Carina [Verfasser]. "Targeting endocardial fibroelastosis in patients with hypoplastic left heart syndrome : a cell culture model / Carina Vorisek". Gießen : Universitätsbibliothek, 2018. http://d-nb.info/1156851327/34.

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Pandurangi, Sindhu. "Comparison of Postoperative Respiratory Function in Neonates with Hypoplastic Left Heart Syndrome Following First Stage Palliation". Thesis, The University of Arizona, 2016. http://hdl.handle.net/10150/603659.

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A Thesis submitted to The University of Arizona College of Medicine - Phoenix in partial fulfillment of the requirements for the Degree of Doctor of Medicine.
Purpose Available surgical procedures in the first stage of the palliation of hypoplastic left heart syndrome (HLHS) are currently the Norwood procedure with Blalock‐Taussing (BT) shunt, Norwood with a Sano shunt (5.0 mm right ventricular‐pulmonary artery conduit), or a hybrid procedure combining surgical pulmonary artery band placement and catheter‐based closure of the ductus arteriosus. Following any of the three procedures, it is necessary for patients to be mechanically ventilated for a period of time; however, little is known about the differences in pulmonary function and outcome among the three groups. Methods We conducted a retrospective chart review of 14 neonates who underwent stage 1 palliation for HLHS, by hybrid procedure or Norwood procedure with BT or Sano shunts, at Phoenix Children’s Hospital from September 2013‐December 2014. Demographic, hemodynamic, and outcome information was collected. Heart rate, respiratory rate, mean arterial pressure, end tidal carbon dioxide (ETCO2), cerebral and renal somatic oximetry, mean airway pressure, ratio of partial pressure of arterial oxygen to inspired oxygen (PaO2/FiO2), partial pressure of arterial carbon dioxide (PaCO2), dead space fraction (Vd/Vt), and dynamic compliance were measured preoperatively, postoperatively, and at multiple time points from 6 to 120 hours postoperatively. Respiratory data was collected using the NM3 monitor (Philips Respironics, Pittsburgh, PA). Outcome measures collected included maximum postoperative lactate, time to extubation, hospital length of stay, and mortality. Results Of the 14 patients, 7 received the Norwood with BT shunt, 5 received the Sano shunt, and 2 received the hybrid procedure. Through linear regression analysis of groups stratified by shunt size, we found that the Vd/Vt ratios of the Sano and 3.0 mm BT shunt groups were higher at earlier times points, but became indistinguishable by 48 hours postoperatively (p=0.02). Linear regression of the 3 surgical groups comparing Vd/Vt across all times points did not show any significant differences (p = 0.79). Linear regression of dynamic compliance among the three groups across all time points also was not significant (p = 0.72). No significant difference was observed in dynamic compliance across all time points when groups were stratified by shunt size (p = 0.33). Examining differences between BT and Sano groups at each time point from 0‐ 120 hours postoperatively using Mann Whitney U analysis did not reveal significance. Analysis of outcomes of length of mechanical ventilation (p=0.61), hospital length of stay (p =0.99), and mortality (p>0.99) also did not differ significantly among the 3 surgical groups. Conclusion Our study identified that the 3.0 mm BT and Sano shunt group had higher Vd/Vt ratios throughout the first 48 postoperative hours. No other differences were found in Vd/Vt or dynamic compliance when surgical groups or shunt sizes were compared. Despite the early differences noted, lack of differences in outcome measures suggests that these early differences have little influence on prognosis.

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Libros sobre el tema "Hypoplastic heart syndromes"

1

Rychik, Jack y Gil Wernovsky, eds. Hypoplastic Left Heart Syndrome. Boston, MA: Springer US, 2003. http://dx.doi.org/10.1007/978-1-4615-0253-1.

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1959-, Rychik Jack y Wernovsky Gil 1956-, eds. Hypoplastic left heart syndrome. Boston: Kluwer Academic Pub., 2003.

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3

Qiao, Bin, Zhong Min Liu, Yu Guo Weng y Ajit P. Yoganathan, eds. Surgical Atlas of Functional Single Ventricle and Hypoplastic Left Heart Syndrome. Singapore: Springer Singapore, 2018. http://dx.doi.org/10.1007/978-981-10-8435-5.

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Wernovsky, Gil y Jack Rychik. Hypoplastic Left Heart Syndrome. Springer London, Limited, 2012.

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Navaratnam, M. y C. Ramamoorthy. Hypoplastic Left Heart Syndrome. Editado por Kirk Lalwani, Ira Todd Cohen, Ellen Y. Choi y Vidya T. Raman. Oxford University Press, 2018. http://dx.doi.org/10.1093/med/9780190685157.003.0009.

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Approximately 960 babies are born per year in the United States with hypoplastic left heart syndrome. Over the last 20 years, advances in surgical techniques, perioperative care, cardiopulmonary bypass, and intensive care unit management have converted this previously fatal condition to one with a neonatal survival rate of 90% to 92% for standard risk patients. Understanding the factors affecting the balance of pulmonary blood flow and systemic blood flow and ensuring adequate cardiac output and end-organ perfusion is critical to successful outcomes. Extracorporeal membrane oxygenation remains an important support modality following stage I palliation. This chapter discusses this syndrome and describes treatment options.

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Hypoplastic Left Heart Syndrome. London: Springer-Verlag, 2005. http://dx.doi.org/10.1007/b138429.

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Wernovsky, Gil y Jack Rychik. Hypoplastic Left Heart Syndrome. Springer London, Limited, 2012.

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Anderson, Robert H., Marco Pozzi y Suzie Hutchinson. Hypoplastic Left Heart Syndrome. Springer London, Limited, 2005.

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9

Hennein, Hani A. y Edward L. Bove. Hypoplastic Left Heart Syndrome. Wiley & Sons, Incorporated, John, 2008.

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(Editor), Hani A. Hennein y Edward L. Bove (Editor), eds. Hypoplastic Left Heart Syndrome. Blackwell Publishing Limited, 2002.

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Capítulos de libros sobre el tema "Hypoplastic heart syndromes"

1

Lintermans, J. P. "Hypoplastic heart syndromes". En Two-dimensional Echocardiography in Infants and Children, 163–80. Dordrecht: Springer Netherlands, 1986. http://dx.doi.org/10.1007/978-94-009-4249-3_11.

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Corno, Antonio F. "Hypoplastic left heart syndrome". En Congenital Heart Defects, 137–45. Heidelberg: Steinkopff, 2003. http://dx.doi.org/10.1007/978-3-642-57358-3_17.

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Freedom, R. M., L. N. Benson y J. F. Smallhorn. "Hypoplastic Left Heart Syndrome". En Neonatal Heart Disease, 333–56. London: Springer London, 1992. http://dx.doi.org/10.1007/978-1-4471-1814-5_21.

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Hinton, Robert B. y D. Woodrow Benson. "Hypoplastic Left Heart Syndrome". En Pediatric Cardiovascular Medicine, 523–33. Oxford, UK: Wiley-Blackwell, 2012. http://dx.doi.org/10.1002/9781444398786.ch38.

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Pizarro, C. y W. I. Norwood. "Hypoplastic Left Heart Syndrome". En Surgery for Congenital Heart Defects, 559–71. Chichester, UK: John Wiley & Sons, Ltd, 2006. http://dx.doi.org/10.1002/0470093188.ch41.

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Chauhan, Monika, Susan Tourner y Christopher W. Mastropietro. "Hypoplastic Left Heart Syndrome". En Cardiac Emergencies in Children, 33–49. Cham: Springer International Publishing, 2018. http://dx.doi.org/10.1007/978-3-319-73754-6_3.

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Hofbeck, Michael, Karl-Heinz Deeg y Thomas Rupprecht. "Hypoplastic Left Heart Syndrome". En Doppler Echocardiography in Infancy and Childhood, 271–82. Cham: Springer International Publishing, 2017. http://dx.doi.org/10.1007/978-3-319-42919-9_20.

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Barron, David J. "Hypoplastic Left Heart Syndrome". En Cardiac Surgery, 923–31. Cham: Springer International Publishing, 2020. http://dx.doi.org/10.1007/978-3-030-24174-2_102.

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Hirsch, Jennifer C., Eric J. Devaney, Richard G. Ohye y Edward L. Bove. "Hypoplastic Left Heart Syndrome". En Pediatric Cardiac Surgery, 619–35. Oxford, UK: Blackwell Publishing Ltd, 2013. http://dx.doi.org/10.1002/9781118320754.ch31.

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Hraška, Viktor y Peter Murín. "Hypoplastic Left Heart Syndrome". En Surgical Management of Congenital Heart Disease II, 39–79. Berlin, Heidelberg: Springer Berlin Heidelberg, 2015. http://dx.doi.org/10.1007/978-3-662-44070-4_2.

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Actas de conferencias sobre el tema "Hypoplastic heart syndromes"

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Jalali, Ali, C. Nataraj, Gerard F. Jones y Daniel J. Licht. "Computational Modeling of Hypoplastic Left Heart Syndrome (HLHS) in Newborn Babies". En ASME 2011 International Design Engineering Technical Conferences and Computers and Information in Engineering Conference. ASMEDC, 2011. http://dx.doi.org/10.1115/detc2011-48825.

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Hypoplastic left heart syndrome (HLHS) is a congenital heart defect (CHD) in which left side of the heart is severely underdeveloped. To better understand this unique physiology, a computational model of the hypoplastic heart was constructed on the basis of compartmental analysis. Lumped parameter model of HLHS is developed based on the electrical circuit analogy. Model is made up of three parts: hypoplastic heart, pulmonary circulation and systemic circulation. Plots of blood pressure and flow for various parts of body show great match between predicted values and what we expected for the case of HLHS babies. Influence of patent ductus arteriosus (PDA) and ASD resistances on cardiac output and pulmonary to systemic flow was also studied. Results show that by increasing the PDA resistance causes more flow to pulmonary compartments and so the ratio increases. Blood flow increases by decreasing of pulmonary artery resistant. Increasing the PDA resistance causes decrease the cardiac output because of more resistance against blood occurs. Saturation increases by decreasing of pulmonary artery resistant.

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Jalali, Ali y C. Nataraj. "A cycle-averaged model of hypoplastic left heart syndrome (HLHS)". En 2011 33rd Annual International Conference of the IEEE Engineering in Medicine and Biology Society. IEEE, 2011. http://dx.doi.org/10.1109/iembs.2011.6090030.

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Kusiak, Andrew, Christopher A. Caldarone, Michael D. Kelleher, Fred S. Lamb, Thomas J. Persoon, Yuan Gan y Alex Burns. "Mining temporal data sets: hypoplastic left heart syndrome case study". En AeroSense 2003, editado por Belur V. Dasarathy. SPIE, 2003. http://dx.doi.org/10.1117/12.487263.

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Buljević, Viktorija Ana, Andrea Dasović Buljević, Dorotea Bartoniček, Dalibor Šarić y Daniel Dilber. "182 Twenty years of hypoplastic left heart syndrome in Croatia". En 10th Europaediatrics Congress, Zagreb, Croatia, 7–9 October 2021. BMJ Publishing Group Ltd and Royal College of Paediatrics and Child Health, 2021. http://dx.doi.org/10.1136/archdischild-2021-europaediatrics.182.

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Alser, Maha W., Huseyin Enes Salman y Huseyin Cagatay Yalcin. "Altered Inflow Hemodynamics affects Heart Development in a Side Specific Manner in the Embryonic Heart". En Qatar University Annual Research Forum & Exhibition. Qatar University Press, 2020. http://dx.doi.org/10.29117/quarfe.2020.0172.

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Background: Hemodynamics, forces from the flowing blood in the heart, is a major epigenetic factor for heart development. Disturbed hemodynamics were shown to induce cardiac malformations in the embryonic heart. Clinically relevant congenital heart defects (CHDs) can be introduced surgically in the lab by disturbing the hemodynamics, like Hypoplastic left heart syndrome (HLHS), characterized by underdeveloped left ventricle is underdeveloped. Left atrial ligation (LAL) on chick embryo is an experimental technique to produce a HLHS-like phenotype. Aims: To reveal mechanobiological mechanisms associated with disturbed hemodynamics that influence the progression of left ventricular hypoplasia using chick embryo model. We also introduce a new technique which we called right atrial ligation (RAL), to examine effect of flow disturbance in right heart. Methods: We combined multiple novel techniques in this research: Heart function was assessed via Echocardiography. Computational fluid dynamics (CFD) analysis was adapted for detailed hemodynamics assessment, such as wall shear stress and blood flow patterns. Heart morphology was assessed by histology, and micro-CT. Results: Echocardiography and CFD analysis showed flow and WSS levels decreased for the flow constricted side resulting in the flow diversion to the opposite side: LAL diverted flow to right side and RAL to left side. This disturbance resulted in underdevelopment of left heart (valve and ventricle) in LAL and underdevelopment of right heart in RAL, revealed with histology and micro-CT. Left side was affected more compared to right side, demonstrating higher plasticity in left heart. Conclusion: This study indicates the critical importance of altered inflow hemodynamics in cardiac development specifically valve and ventricle development. Our comprehensive approach can be used to predict the initiation and growth of congenital heart defects.

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D'Avenio, Giuseppe, Aurelio Secinaro, Antonio Amodeo y Mauro Grigioni. "Patient-specific Fluid Dynamical Evaluation of Hypoplastic Left Heart Syndrome Surgical Treatment". En 2020 IEEE 20th Mediterranean Electrotechnical Conference ( MELECON). IEEE, 2020. http://dx.doi.org/10.1109/melecon48756.2020.9140649.

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Nasr, Amal, Aya Omar, Maha Alser, Huseyin Yalcin y Fatiha Benslimane. "Unraveling Gene Expression Profiles of Cardiac Genes that Participate in Embryonic development of Congenital Heart Defects using Chick Embryo". En Qatar University Annual Research Forum & Exhibition. Qatar University Press, 2020. http://dx.doi.org/10.29117/quarfe.2020.0196.

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Hypoplastic left heart syndrome (HLHS) is a rare but serious subtype of congenital heart defect (CHDs) at which the hemodynamics are disturbed. In this project, HLHS was introduced surgically by left atrial ligation (LAL) to embryonic chicks and the subsequent effects of it were studied. Different tests were done post-LAL to study cardiac morphology, function, and gene expression of cardiac markers.

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Qian, Y., J. L. Liu, M. Umezu, K. Itatani y K. Miyaji. "A Study of Surgical Optimization for Congenital Heart Diseases Based on Computational Hemodynamic Analysis". En ASME 2009 Summer Bioengineering Conference. American Society of Mechanical Engineers, 2009. http://dx.doi.org/10.1115/sbc2009-206443.

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Hypoplastic left heart syndrome (HLHS) is one kind of serious congenital heart diseases (CHD). With a small, underdeveloped left ventricle, a heart suffering from HLHS cannot effectively supply enough blood flow to provide for the needs of the body. In order to improve blood circulation, surgery for HLHS has to be carried out at a very early stage. In general, three-stage palliative surgical management for newborns is now widely accepted [1, 2]; Norwood, Glenn, and Fontan.

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Punithakumar, K., N. Tahmasebi, P. Boulanger y M. Noga. "Convolutional Neural Network Based Automated RV Segmentation for Hypoplastic Left Heart Syndrome MRI". En 8th International Conference of Pattern Recognition Systems (ICPRS 2017). Institution of Engineering and Technology, 2017. http://dx.doi.org/10.1049/cp.2017.0158.

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Zhang, Xiaojun, Yun Cheng y Xiaoyang Li. "Numerical simulation of blood flow in Blalock-Taussig Shunt for hypoplastic left heart syndrome". En 2011 IEEE International Conference on Mechatronics and Automation (ICMA). IEEE, 2011. http://dx.doi.org/10.1109/icma.2011.5985666.

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